Rapid progression of neuromuscular disorder related cardiomyopathy in a young patient.
Intern Med
; 52(24): 2771-5, 2013.
Article
in En
| MEDLINE
| ID: mdl-24334583
ABSTRACT
An 11-year and 3-month-old boy with a neuromuscular disorder was admitted for dyspnea. Echocardiography revealed severe left ventricular dysfunction with an ejection fraction (EF) of 17%. However, the EF had been 57% when the patient was 10 years and 9 months old. The patient's clinical condition became refractory, and he died on the 155th day of hospitalization. Speckle-tracking analysis was retrospectively performed, which demonstrated that the global radial strain was within the normal range; however, the global longitudinal and circumferential strains were lower -than -normal 10 years and 9 months of age. Adult neuromuscular disorder-related secondary cardiomyopathy generally progresses slowly, although progression depends on the age of onset of cardiomyopathy.
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Database:
MEDLINE
Main subject:
Disease Progression
/
Cardiomyopathies
/
Neuromuscular Diseases
Limits:
Child
/
Humans
/
Male
Language:
En
Year:
2013
Type:
Article