Long-term outcome for kaposiform hemangioendothelioma: A report of two cases.
Pediatr Blood Cancer
; 64(2): 284-286, 2017 02.
Article
in En
| MEDLINE
| ID: mdl-27701822
ABSTRACT
Kaposiform hemangioendothelioma (KHE) is a rare aggressive vascular tumor of skin and deep soft tissues that typically presents in infancy and may be associated with a potentially life-threatening coagulopathy known as Kasabach-Merrit phenomenon (KMP). Recent advances in medical therapy have successfully treated many patients. However, our knowledge regarding the natural history of these lesions and optimum surveillance strategies remains rudimentary. We report two young women who had KHE with KMP treated in infancy and presented in adolescence with comorbidities related to their KHE tumor. This presentation supports the need for long-term surveillance in these patients.
Key words
Full text:
1
Database:
MEDLINE
Main subject:
Sarcoma, Kaposi
/
Kasabach-Merritt Syndrome
/
Hemangioendothelioma
Type of study:
Prognostic_studies
Limits:
Female
/
Humans
/
Infant
Language:
En
Year:
2017
Type:
Article