Lung Manifestations of IgG4-related Disease. A multifaceted disorder. Presentation of two cases and short review of the literature.
Sarcoidosis Vasc Diffuse Lung Dis
; 35(1): 74-80, 2018.
Article
in En
| MEDLINE
| ID: mdl-32476883
ABSTRACT
Immunoglobulin (Ig) G4-related disease (IgG4-RD) is a recently described systemic inflammatory disease associated with elevated circulating levels of IgG4. IgG4-RD may affect one or more organs and lesions can present synchronously or metachronously in different organs. Pulmonary involvement of IgG4-related disease includes airway, lung parenchyma, pleura and mediastinum. In this article, we report two cases of IgG4-RD to show the multifaceted manifestations of this disease in the lungs. (Sarcoidosis Vasc Diffuse Lung Dis 2018; 35 74-80).