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Spinal Dural Arteriovenous Fistula: A Mimic of Demyelinating Disease and Radiculopathy.
Alfaro-Olivera, María; Otiniano-Sifuentes, Ricardo D; Simbrón-Ribbeck, Lourdes; Zelada-Ríos, Laura; Barrientos-Imán, Danny; Abanto, Carlos; Ramírez-Quiñones, Jorge; Valencia, Ana.
Afiliación
  • Alfaro-Olivera M; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Otiniano-Sifuentes RD; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Simbrón-Ribbeck L; Departamento de Diagnóstico por Imágenes, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Zelada-Ríos L; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Barrientos-Imán D; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Abanto C; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Ramírez-Quiñones J; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
  • Valencia A; Department of Neurovascular Diseases, Instituto Nacional de Ciencias Neurológicas, Lima, PER.
Cureus ; 14(4): e24134, 2022 Apr.
Article en En | MEDLINE | ID: mdl-35573541
ABSTRACT
Spinal dural arteriovenous fistula (SDAVF) is characterized by an abnormal connection between a radicular artery and the venous plexus producing spinal cord venous congestion. It manifests with nonspecific sensory and motor symptoms. We present three cases of SDAVF with different forms of presentation; in two cases, an autoimmune etiology was considered, and in the third case, the initial diagnosis was chronic radiculopathy. In all three cases, a serpentine enhancement was observed after the gadolinium in the dorsal region of the spinal cord corresponded to flow voids in T2-weighted images, which guided the diagnosis. SDAVF should be considered in atypical clinical presentations of radiculopathies or spinal cord syndromes, especially spinal conus or epicone syndrome. Likewise, it should be part of the differential diagnosis of spinal cord presentations of demyelinating diseases such as multiple sclerosis or neuromyelitis optica spectrum disorders.
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