ABSTRACT
The aim of this article is to describe the care of a patient with fibrodysplasia ossificans progressiva (FOP) and to provide dentists with a guide for how to safely care for patients with FOP. Treatment improved the patient's limited mouth opening. FOP is a rare autosomal dominant disorder characterized by congenital malformation of the fingers and toes by heterotopic ossification progressiva of the connective tissue. This ossification causes a limitation in osteoradicular mobility, mainly affecting the spine, shoulders, hips, and peripheral joints. The disease can manifest from pregnancy until adulthood, with no greater prevalence associated with race or gender. Although rare, the disease can be easily identified by its clinical features, and diagnosis can be confirmed by a radiographic examination. There is no known effective treatment for this disease. All therapeutic treatment must be conservative to avoid any condition that may cause heterotopic ossification. Guidelines to prevent new ossifications are important for patients with FOP. Dental professionals should be cautious in planning treatment, avoiding anesthesia, especially in the mandible, to prevent ankylosis of the temporo-mandibular joints. The prevention of dental caries is essential to avoid the need for more invasive treatment.
Subject(s)
Myositis Ossificans/therapy , Range of Motion, Articular/physiology , Temporomandibular Joint Disorders/therapy , Ankylosis/prevention & control , Calcinosis/diagnosis , Exercise Therapy/instrumentation , Humans , Myofunctional Therapy/instrumentation , Myositis Ossificans/diagnosis , Ossification, Heterotopic/diagnosis , Temporomandibular Joint Disorders/prevention & controlABSTRACT
A correlação entre manifestações otológicas e desordens temporomandibulares tem sido um assunto de grande pesquisa e controvérsia na literatura. Dentre os sintomas otológicos relatados por pacientes portadores de DTM, a otalgia merece destaque por sua importância clínica como queixa do paciente. Algumas explicações da base anatômica e fisiológica tentam elucidar esta correlação, porém muitas são refutadas e desconsideradas. Apesar da polêmica e das diversas teorias sobre o assunto, realizou-se uma revisão da literatura sobre as possíveis explicações para a sensação de otalgia, muitas vezes relatada por pacientes que apresentam desordens temporomandibulares