RESUMO
Multiple lymphomatous polyposis is a rare type of intestinal lymphoma characterized by non-Hodgkin's lymphoma of follicular mantle cell origin and extremely poor prognosis. We report a case of systemic lymphoma with the intestinal involvement of multiple lymphomatous polyposis. Although radiographic and endoscopic features of the case were compatible with multiple lymphomatous polyposis, histologic evidence suggested the diagnosis of diffuse large cell lymphoma rather than mantle cell lymphoma. Our case seems to be unique in its histologic findings and also in its prognosis, because the patient has been alive for more than 50 months after diagnosis.
Assuntos
Neoplasias Intestinais/patologia , Pólipos Intestinais/patologia , Linfoma/patologia , Protocolos de Quimioterapia Combinada Antineoplásica , Sulfato de Bário , Biópsia , Colonoscopia , Ciclofosfamida/administração & dosagem , Doxorrubicina/administração & dosagem , Enema , Humanos , Neoplasias Intestinais/diagnóstico por imagem , Pólipos Intestinais/diagnóstico por imagem , Linfoma/diagnóstico por imagem , Masculino , Pessoa de Meia-Idade , Prednisolona/administração & dosagem , Radiografia , Vincristina/administração & dosagemRESUMO
The patient, an 18-yr-old male (admission ht 153 cm, wt 30 kg), had been suffering from growth arrest and intermittent abdominal pain since he was 13 yr old, which was left untreated. Examinations on admission disclosed almost normal pituitary function, while levels of testosterone and somatomedin C were low. Roentgenological examination revealed extensive skip-stenotic lesions and longitudinal ulcers in the ileum, diagnostic of Crohn's disease. Therapy involving high-caloric parenteral and enteral alimentation resulted in a marked increase in both ht and wt, and improvement in roentgenological and colonoscopical findings. The interrelation between Crohn's disease and malnutrition with reference to some reports in the literature is discussed.