N-butyldeoxynojirimycin delays motor deficits, cerebellar microgliosis, and Purkinje cell loss in a mouse model of mucolipidosis type IV.
Neurobiol Dis
; 105: 257-270, 2017 Sep.
Article
in En
| MEDLINE
| ID: mdl-28610891
Key words
Full text:
1
Database:
MEDLINE
Therapeutic Methods and Therapies TCIM:
Terapias_biologicas
/
Aromoterapia
Main subject:
Purkinje Cells
/
Cerebellum
/
1-Deoxynojirimycin
/
Enzyme Inhibitors
/
Gliosis
/
Movement Disorders
/
Mucolipidoses
Type of study:
Etiology_studies
/
Prognostic_studies
Language:
En
Journal:
Neurobiol Dis
Year:
2017
Type:
Article
Affiliation country:
United States