Bioenergetics dysfunction, mitochondrial permeability transition pore opening and lipid peroxidation induced by hydrogen sulfide as relevant pathomechanisms underlying the neurological dysfunction characteristic of ethylmalonic encephalopathy.
Biochim Biophys Acta Mol Basis Dis
; 1863(9): 2192-2201, 2017 09.
Article
in En
| MEDLINE
| ID: mdl-28624490
Key words
Full text:
1
Database:
MEDLINE
Therapeutic Methods and Therapies TCIM:
Terapias_energeticas
/
Bioenergetica
Main subject:
Purpura
/
Lipid Peroxidation
/
Cerebral Cortex
/
Brain Diseases, Metabolic, Inborn
/
Mitochondrial Membrane Transport Proteins
/
Energy Metabolism
/
Hydrogen Sulfide
Language:
En
Journal:
Biochim Biophys Acta Mol Basis Dis
Year:
2017
Type:
Article
Affiliation country:
Brazil