Fat-soluble vitamins in infants identified by cystic fibrosis newborn screening.
Pediatr Pulmonol Suppl
; 7: 52-5, 1991.
Article
en En
| MEDLINE
| ID: mdl-1782131
ABSTRACT
Fat-soluble vitamin status was assessed in 36 infants diagnosed with cystic fibrosis by newborn screening in the Colorado Program. At the time of diagnosis of cystic fibrosis, 36% of infants were hypoalbuminemic, 21% had vitamin A deficiency, 35% had vitamin D deficiency, and 38% had vitamin E deficiency. None had vitamin K deficiency. Supplementation with pancreatic enzymes, a multiple vitamin preparation, and additional vitamin E was associated with normalization of serum albumin, retinol, and 25-hydroxyvitamin D and negative PIVKA testing at age 6 and 12 months. Several patients remained vitamin E deficient, but this was felt to be due to poor compliance. Biochemical evidence of fat-soluble vitamin deficiency is common before age 3 months in infants with CF and responds to supplementation in the first year of life.
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Bases de datos:
MEDLINE
Asunto principal:
Deficiencia de Vitamina A
/
Deficiencia de Vitamina D
/
Deficiencia de Vitamina E
/
Tamizaje Neonatal
/
Fibrosis Quística
Tipo de estudio:
Diagnostic_studies
/
Screening_studies
Idioma:
En
Revista:
Pediatr Pulmonol Suppl
Año:
1991
Tipo del documento:
Article