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Medium-chain triglycerides supplement therapy with a low-carbohydrate formula can supply energy and enhance ammonia detoxification in the hepatocytes of patients with adult-onset type II citrullinemia.
Hayasaka, Kiyoshi; Numakura, Chikahiko; Yamakawa, Mitsunori; Mitsui, Tetsuo; Watanabe, Hisayoshi; Haga, Hiroaki; Yazaki, Masahide; Ohira, Hiromasa; Ochiai, Yasuo; Tahara, Toshiyuki; Nakahara, Tamio; Yamashiki, Noriyo; Nakayama, Takahiro; Kon, Takashi; Mitsubuchi, Hiroshi; Yoshida, Hiroshi.
Afiliación
  • Hayasaka K; Department of Pediatrics, Yamagata University School of Medicine, 2-2-2 Iida-nishi, Yamagata, 990-9585, Japan. hayasaka@med.id.yamagata-u.ac.jp.
  • Numakura C; Department of Pediatrics, Miyukikai Hospital, Kaminoyama, Japan. hayasaka@med.id.yamagata-u.ac.jp.
  • Yamakawa M; Department of Pediatrics, Yamagata University School of Medicine, 2-2-2 Iida-nishi, Yamagata, 990-9585, Japan.
  • Mitsui T; Department of Pathological Diagnostics, Yamagata University School of Medicine, Yamagata, Japan.
  • Watanabe H; Department of Pediatrics, Yamagata University School of Medicine, 2-2-2 Iida-nishi, Yamagata, 990-9585, Japan.
  • Haga H; Department of Gastroenterology, Yamagata University School of Medicine, Yamagata, Japan.
  • Yazaki M; Department of Gastroenterology, Yamagata University School of Medicine, Yamagata, Japan.
  • Ohira H; Department of Biological Sciences for Intractable Neurological Disorders, Institute for Biomedical Sciences, Shinshu University, Nagano, Japan.
  • Ochiai Y; Department of Gastroenterology, Fukushima Medical University School of Medicine, Fukushima, Japan.
  • Tahara T; Department of Gastroenterology, Saiseikai Utsunomiya Hospital, Tochigi, Japan.
  • Nakahara T; Department of Gastroenterology, Saiseikai Utsunomiya Hospital, Tochigi, Japan.
  • Yamashiki N; Department of Gastroenterology, Hikone Municipal Hospital, Hikone, Shiga, Japan.
  • Nakayama T; Organ Transplantation Unit, Kyoto University, Kyoto, Japan.
  • Kon T; Division of Internal Medicine, Nihonkai General Hospital, Sakata, Japan.
  • Mitsubuchi H; Department of Gastroenterology, Yonezawa Municipal Hospital, Yonezawa, Japan.
  • Yoshida H; Department of Pediatrics, Graduate School of Medical Sciences, Kumamoto University, Kumamoto, Japan.
J Inherit Metab Dis ; 41(5): 777-784, 2018 09.
Article en En | MEDLINE | ID: mdl-29651749

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Triglicéridos / Carbohidratos / Encefalopatía Hepática / Citrulinemia / Hiperamonemia Tipo de estudio: Etiology_studies / Prognostic_studies Idioma: En Revista: J Inherit Metab Dis Año: 2018 Tipo del documento: Article País de afiliación: Japón

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Triglicéridos / Carbohidratos / Encefalopatía Hepática / Citrulinemia / Hiperamonemia Tipo de estudio: Etiology_studies / Prognostic_studies Idioma: En Revista: J Inherit Metab Dis Año: 2018 Tipo del documento: Article País de afiliación: Japón