Different outcomes following parathyroidectomy in patients with uremic tumoral calcinosis: two case reports.
BMC Nephrol
; 24(1): 55, 2023 03 15.
Article
en En
| MEDLINE
| ID: mdl-36922797
BACKGROUND: Uremic tumoral calcinosis (UTC) is a rare complication in hemodialysis patients, whose mechanism remains incompletely understood. We report two cases with UTC who experienced completely different patterns of regression following parathyroidectomy, although there were no significant differences in serum calcium levels, parathyroid hormone, or phosphorus production between the two patients. CASE PRESENTATION: Case 1 had a substantial improvement in soft tissue calcification. However, in Case 2, one calcified mass was partially absorbed, while the others were aggravated with severe microvascular calcification and subcutaneous extravascular calcification. Whole-exome sequencing data revealed five mutation sites associated with atherosclerosis. CONCLUSION: The different outcomes in UTC patients after PTX are rare. Further studies are required to elucidate the mechanism of paradoxical changes occurring in patients with UTC after parathyroidectomy.
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Texto completo:
1
Bases de datos:
MEDLINE
Asunto principal:
Calcinosis
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Hiperparatiroidismo Secundario
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Fallo Renal Crónico
Tipo de estudio:
Etiology_studies
Idioma:
En
Revista:
BMC Nephrol
Año:
2023
Tipo del documento:
Article
País de afiliación:
China