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Biomarkers of oxidative stress, inflammation, and vascular dysfunction in inherited cystathionine ß-synthase deficient homocystinuria and the impact of taurine treatment in a phase 1/2 human clinical trial.
Van Hove, Johan L K; Freehauf, Cynthia L; Ficicioglu, Can; Pena, Loren D M; Moreau, Kerrie L; Henthorn, Thomas K; Christians, Uwe; Jiang, Hua; Cowan, Tina M; Young, Sarah P; Hite, Michelle; Friederich, Marisa W; Stabler, Sally P; Spector, Elaine B; Kronquist, Kathryn E; Thomas, Janet A; Emmett, Peggy; Harrington, Mary J; Pyle, Laura; Creadon-Swindell, Geralyn; Wempe, Michael F; MacLean, Kenneth N.
Afiliação
  • Van Hove JLK; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Freehauf CL; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Ficicioglu C; Division of Human Genetics, The Children's Hospital Philadelphia, Perelman School of Medicine at the University of Pennsylvania, Philadelphia, Pennsylvania.
  • Pena LDM; Division of Medical Genetics, Department of Pediatrics, Duke University, Durham, North Carolina.
  • Moreau KL; Department of Medicine, School of Medicine, University of Colorado, Aurora, Colorado.
  • Henthorn TK; Geriatric Research and Education Center, Denver Veterans Administration Medical Center, Aurora, Colorado.
  • Christians U; iC42 Clinical Research and Development, Department of Anesthesiology, School of Medicine, University of Colorado, Aurora, Colorado.
  • Jiang H; Skaggs School of Pharmacy and Pharmaceutical Sciences, University of Colorado, Aurora, Colorado.
  • Cowan TM; iC42 Clinical Research and Development, Department of Anesthesiology, School of Medicine, University of Colorado, Aurora, Colorado.
  • Young SP; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Hite M; Department of Pathology, Stanford University, Stanford, California.
  • Friederich MW; Division of Medical Genetics, Department of Pediatrics, Duke University, Durham, North Carolina.
  • Stabler SP; Research Institute, Children's Hospital Colorado, Aurora, Colorado.
  • Spector EB; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Kronquist KE; Department of Medicine, School of Medicine, University of Colorado, Aurora, Colorado.
  • Thomas JA; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Emmett P; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Harrington MJ; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • Pyle L; CTRC Core Laboratory, Children's Hospital Colorado, Aurora, Colorado.
  • Creadon-Swindell G; CTRC Core Laboratory, Children's Hospital Colorado, Aurora, Colorado.
  • Wempe MF; Department of Pediatrics, School of Medicine, University of Colorado, Aurora, Colorado.
  • MacLean KN; Department of Biostatistics and Informatics, Colorado School of Public Health, University of Colorado, Aurora, Colorado.
J Inherit Metab Dis ; 42(3): 424-437, 2019 05.
Article em En | MEDLINE | ID: mdl-30873612

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Taurina / Biomarcadores / Cistationina beta-Sintase / Homocistinúria Tipo de estudo: Clinical_trials País/Região como assunto: America do norte Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2019 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Taurina / Biomarcadores / Cistationina beta-Sintase / Homocistinúria Tipo de estudo: Clinical_trials País/Região como assunto: America do norte Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2019 Tipo de documento: Article