Asunto(s)
Síndrome de Horner/diagnóstico , Venas Yugulares/diagnóstico por imagen , Trombosis de la Vena/diagnóstico , Antiinfecciosos/administración & dosificación , Cefuroxima/administración & dosificación , Cefuroxima/análogos & derivados , Quimioterapia Combinada , Síndrome de Horner/etiología , Humanos , Imagen por Resonancia Magnética , Masculino , Metronidazol/administración & dosificación , Persona de Mediana Edad , Flebografía , Enfermedades de la Glándula Submandibular/complicaciones , Enfermedades de la Glándula Submandibular/diagnóstico , Enfermedades de la Glándula Submandibular/tratamiento farmacológico , Ultrasonografía Doppler en Color , Trombosis de la Vena/complicacionesRESUMEN
The spectrum of optic neuromyelitis (ONM) ranges from monophasic or recurrent idiopathic forms of the disease, to ONM associated with autoimmune disorders. A distinct form of the disease, called recurrent ONM with endocrinopathies, characterized by spinal cord involvement (cavitations with syringomyeloid sensory disturbance), rapid evolution to blindness and paraplegia, characteristic cerebrospinal fluid (CSF) findings, and association with hypothalamus-pituitary dysfunction, has recently been described. The first case of ONM with endocrinopathies in a female Caucasian from Europe is presented, supporting the existence of this syndrome as a separate entity.
Asunto(s)
Enfermedades del Sistema Endocrino/complicaciones , Neuromielitis Óptica/complicaciones , Adulto , Enfermedades del Sistema Endocrino/patología , Femenino , Humanos , Imagen por Resonancia Magnética/métodos , Neuromielitis Óptica/patología , RecurrenciaRESUMEN
A new computerized method is described for measuring parkinsonian rigidity with an elbow device. We present data from 127 subjects (103 controls and 24 parkinsonian patients) to show the clinical utility of the method. The instrumental quantification of rigidity correlates highly with clinical ratings of parkinsonian rigidity. The test-retest repeatability was excellent. In parkinsonian patients versus normal controls, significantly higher values of measured rigidity were observed. Moreover, activation procedure significantly increases rigidity only in parkinsonian patients. Activated rigidity in control subjects is lower than basal values. The procedure was sensitive to increased rigidity in parkinsonian patients during 3 days' drug holiday. Contrary to previous reports, levodopa therapy reduced both basal and activated rigidity in parkinsonian patients. This method is relatively simple and takes only 15 min to complete.