RESUMEN
BACKGROUND: Although parenteral nutrition (PN) significantly improves mortality rates in pediatric short bowel syndrome (SBS), long-term PN has many possible complications and impacts quality of life. Bowel lengthening procedures (BLPs) increase the contact surface of food and the intestinal mucosa and enable the better absorption of nutrients and liquids, possibly leading to a PN decrease. METHODS: We retrospectively reviewed the data of patients with short bowel syndrome who underwent BLPs in the period from January 2016 to January 2022. Overall, eight patients, four male, five born prematurely, underwent BLPs. RESULTS: There was a significant decrease in the percentage of total caloric intake provided via PN and PN volume after the BLPs. The more evident results were seen 6 months after the procedure and at the last follow-up, which was, on average, 31 months after the procedure. Two patients were weaned off PN after their BLPs. Patients remained well nourished during the follow-up. CONCLUSIONS: The BLP led to a significant decrease in PN needs and an increase in the food intake; however, significant changes happened more than 6 months after the procedure.
Asunto(s)
Nutrición Parenteral , Síndrome del Intestino Corto , Humanos , Síndrome del Intestino Corto/cirugía , Síndrome del Intestino Corto/terapia , Masculino , Femenino , Estudios Retrospectivos , Resultado del Tratamiento , Lactante , Preescolar , Niño , Estado Nutricional , Ingestión de Energía , Procedimientos Quirúrgicos del Sistema Digestivo/métodos , Procedimientos Quirúrgicos del Sistema Digestivo/efectos adversos , Calidad de VidaRESUMEN
Digital clubbing is most commonly caused by pulmonary or cardiac disease, and only rarely it is a manifestation of a gastroenterological disorder. We report a pediatric patient in whom severe gastroesophageal reflux disease caused anemia and digital clubbing, partial clinical presentation of the Herbst triad.