Erdheim-Chester disease detected with 99mTc MDP bone SPECT/CT.
JBR-BTR
; 95(4): 245-8, 2012.
Article
en En
| MEDLINE
| ID: mdl-23019992
Erdheim-Chester disease (ECD) is a rare non-Langerhans' cell histiocytosis. Mild but permanent juxta-articular bone pain in mainly knees and ankles is the most frequent associated symptom. Despite the pathognomonic radiographic findings, most cases are still diagnosed by the pathologist.The lesions consist of lipid-storing CD 68 +/CD 1a--non-Langerhans' cell histiocytes, most frequently localized in bone but also involving multiple organ systems in the body. We present a case report in which the diagnosis of ECD was established with 99mTc MDP bone SPECT/CT.
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Base de datos:
MEDLINE
Asunto principal:
Huesos
/
Tomografía Computarizada de Emisión de Fotón Único
/
Medronato de Tecnecio Tc 99m
/
Radiofármacos
/
Enfermedad de Erdheim-Chester
Tipo de estudio:
Diagnostic_studies
Idioma:
En
Revista:
JBR-BTR
Año:
2012
Tipo del documento:
Article