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Imbalances in protein homeostasis caused by mutant desmin.
Winter, L; Unger, A; Berwanger, C; Spörrer, M; Türk, M; Chevessier, F; Strucksberg, K-H; Schlötzer-Schrehardt, U; Wittig, I; Goldmann, W H; Marcus, K; Linke, W A; Clemen, C S; Schröder, R.
Afiliación
  • Winter L; Institute of Neuropathology, University Hospital Erlangen, Erlangen, Germany.
  • Unger A; Neuromuscular Research Department, Center for Anatomy and Cell Biology, Medical University of Vienna, Vienna, Austria.
  • Berwanger C; Department of Cardiovascular Physiology, Ruhr-University Bochum, Bochum, Germany.
  • Spörrer M; Institute for Genetics of Heart Diseases, University Hospital Münster, Münster, Germany.
  • Türk M; Department of Neurology, Heimer Institute for Muscle Research, University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.
  • Chevessier F; Center for Biochemistry, Institute of Biochemistry I, Medical Faculty, University of Cologne, Cologne, Germany.
  • Strucksberg KH; Center for Medical Physics and Technology, Biophysics Group, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Schlötzer-Schrehardt U; Department of Neurology, University Hospital Erlangen, Erlangen, Germany.
  • Wittig I; Institute of Neuropathology, University Hospital Erlangen, Erlangen, Germany.
  • Goldmann WH; Center for Biochemistry, Institute of Biochemistry I, Medical Faculty, University of Cologne, Cologne, Germany.
  • Marcus K; Department of Ophthalmology, University Hospital Erlangen, Erlangen, Germany.
  • Linke WA; Functional Proteomics, SFB815 Core Unit, Medical School, Goethe University, Frankfurt, Germany.
  • Clemen CS; Center for Medical Physics and Technology, Biophysics Group, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Schröder R; Medizinisches Proteom-Center, Medical Faculty, Ruhr-University Bochum, Bochum, Germany.
Neuropathol Appl Neurobiol ; 45(5): 476-494, 2019 08.
Article en En | MEDLINE | ID: mdl-30179276

Texto completo: 1 Base de datos: MEDLINE Asunto principal: Músculo Esquelético / Desmina / Proteostasis / Distrofias Musculares / Cardiomiopatías Tipo de estudio: Prognostic_studies Idioma: En Revista: Neuropathol Appl Neurobiol Año: 2019 Tipo del documento: Article

Texto completo: 1 Base de datos: MEDLINE Asunto principal: Músculo Esquelético / Desmina / Proteostasis / Distrofias Musculares / Cardiomiopatías Tipo de estudio: Prognostic_studies Idioma: En Revista: Neuropathol Appl Neurobiol Año: 2019 Tipo del documento: Article