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Biophysical impact of sphingosine and other abnormal lipid accumulation in Niemann-Pick disease type C cell models.
Carreira, Ana C; Pokorna, Sarka; Ventura, Ana E; Walker, Mathew W; Futerman, Anthony H; Lloyd-Evans, Emyr; de Almeida, Rodrigo F M; Silva, Liana C.
Afiliación
  • Carreira AC; iMed.ULisboa - Research Institute for Medicines, Faculdade de Farmácia, Universidade de Lisboa, Av. Prof. Gama Pinto, 1649-003 Lisboa, Portugal; Centro de Química e Bioquímica (CQB) e Centro de Química Estrutural (CQE), Faculdade de Ciências, Universidade de Lisboa, Ed. C8, Campo Grande, 1749-016 Li
  • Pokorna S; Department of Biomolecular Sciences, Weizmann Institute of Science, Rehovot, Israel; Heyrovský Institute of Physical Chemistry of the Czech Academy of Sciences, Dolejskova 3, 182 23 Prague, Czech Republic.
  • Ventura AE; iMed.ULisboa - Research Institute for Medicines, Faculdade de Farmácia, Universidade de Lisboa, Av. Prof. Gama Pinto, 1649-003 Lisboa, Portugal; Department of Biomolecular Sciences, Weizmann Institute of Science, Rehovot, Israel; iBB-Institute for Bioengineering and Biosciences, Department of Bioeng
  • Walker MW; Sir Martin Evans Building, School of Biosciences, Cardiff University, Museum Avenue, Cardiff, UK.
  • Futerman AH; Department of Biomolecular Sciences, Weizmann Institute of Science, Rehovot, Israel.
  • Lloyd-Evans E; Sir Martin Evans Building, School of Biosciences, Cardiff University, Museum Avenue, Cardiff, UK.
  • de Almeida RFM; Centro de Química e Bioquímica (CQB) e Centro de Química Estrutural (CQE), Faculdade de Ciências, Universidade de Lisboa, Ed. C8, Campo Grande, 1749-016 Lisboa, Portugal. Electronic address: rfalmeida@fc.ul.pt.
  • Silva LC; iMed.ULisboa - Research Institute for Medicines, Faculdade de Farmácia, Universidade de Lisboa, Av. Prof. Gama Pinto, 1649-003 Lisboa, Portugal. Electronic address: lianacsilva@ff.ulisboa.pt.
Article en En | MEDLINE | ID: mdl-33892149

Texto completo: 1 Base de datos: MEDLINE Asunto principal: Esfingolípidos / Esfingosina / Enfermedad de Niemann-Pick Tipo C Tipo de estudio: Prognostic_studies Idioma: En Revista: Biochim Biophys Acta Mol Cell Biol Lipids Año: 2021 Tipo del documento: Article

Texto completo: 1 Base de datos: MEDLINE Asunto principal: Esfingolípidos / Esfingosina / Enfermedad de Niemann-Pick Tipo C Tipo de estudio: Prognostic_studies Idioma: En Revista: Biochim Biophys Acta Mol Cell Biol Lipids Año: 2021 Tipo del documento: Article