Radiologically isolated aquaporin-4 antibody neuromyelitis optica spectrum disorder.
Mult Scler
; 28(4): 676-679, 2022 04.
Article
en En
| MEDLINE
| ID: mdl-35332817
ABSTRACT
Aquaporin-4 antibody (AQP4-Ab) Neuromyelitis Optica Spectrum Disorder (NMOSD) is a rare neuroinflammatory syndrome presenting predominantly with optic neuritis and transverse myelitis. We report a case of radiologically isolated longitudinally extensive optic neuritis in an asymptomatic 12-year-old female with positive serum AQP4-Ab, with resolution of imaging changes after immune therapy. By contrast to patients with radiologically isolated syndrome, of which some will never convert to multiple sclerosis, the pathogenicity of AQP4-Ab in the context of sub-clinical disease, supported treatment in our patient. Given the severe morbidity in AQP4-Ab NMOSD, prognostic biomarkers for disease severity are required to guide optimal therapy for patients.
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Texto completo:
1
Base de datos:
MEDLINE
Asunto principal:
Neuritis Óptica
/
Neuromielitis Óptica
Tipo de estudio:
Prognostic_studies
Idioma:
En
Revista:
Mult Scler
Asunto de la revista:
NEUROLOGIA
Año:
2022
Tipo del documento:
Article