Isolated embryonal rhabdomyosarcoma of the anterior petrous bone in a young child: Focusing on the intra-operative diagnosis and differentials.
Clin Neuropathol
; 43(2): 48-52, 2024.
Article
en En
| MEDLINE
| ID: mdl-38085093
ABSTRACT
OBJECTIVE:
Rhabdomyosarcoma is a common soft tissue tumor, but isolated involvement of anterior portion of petrous bone is exceedingly rare. Here, we present a case of embryonal rhabdomyosarcoma involving the anterior petrous without involvement of the mastoid and middle ear. PATIENT A 6-year-old boy presented with a progressive right side lower motor neuron facial paresis for 1-month duration along with headache and recurrent vomiting episodes. Radiology showed a contrast-enhancing lesion involving the right petrous apex. He underwent craniotomy and excision of the lesion. Based on the frozen section, a diagnosis of rhabdomyosarcoma was rendered, and gross total resection could be achieved. Postoperative course was uneventful.CONCLUSION:
Isolated petrous bone involvement of embryonal rhabdomyosarcoma is a rare presentation. Intra-operative frozen section plays a key role in decision making regarding the extent of excision. Hence, a prompt and accurate diagnosis is essential in managing these cases.
Texto completo:
1
Base de datos:
MEDLINE
Asunto principal:
Rabdomiosarcoma
/
Rabdomiosarcoma Embrionario
Idioma:
En
Revista:
Clin Neuropathol
Año:
2024
Tipo del documento:
Article