Sarcoidosis-Associated Pulmonary Hypertension.
Clin Chest Med
; 45(1): 185-197, 2024 03.
Article
en En
| MEDLINE
| ID: mdl-38245366
ABSTRACT
Pulmonary hypertension is a life-threatening complication of advanced sarcoidosis. Many mechanisms can cause an elevation of pulmonary pressure in sarcoidosis, leading to precapillary or postcapillary pulmonary hypertension. Sarcoidosis-associated pulmonary hypertension contributes to severe exertional dyspnea, reduced exercise capacity, and notably compromised the survival. Despite the critical functional and prognostic implications of pulmonary hypertension in sarcoidosis, there is a scarcity of specific guidelines on the management of these patients due to a lack of evidence. Hence, further research is required to identify subgroups of patients who may benefit from pulmonary arterial hypertension-targeted therapies and/or immunosuppressive therapies.
Palabras clave
Texto completo:
1
Base de datos:
MEDLINE
Asunto principal:
Sarcoidosis
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Sarcoidosis Pulmonar
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Hipertensión Arterial Pulmonar
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Hipertensión Pulmonar
Tipo de estudio:
Etiology_studies
/
Guideline
/
Prognostic_studies
/
Risk_factors_studies
Idioma:
En
Revista:
Clin Chest Med
Año:
2024
Tipo del documento:
Article