Heart Transplantation for Uhl Anomaly in an Adult.

Toubat, Omar; Han, Jason J; Predina, Jarrod D; Goldberg, Lee R; Ibrahim, Michael E

Heart Transplantation for Uhl Anomaly in an Adult.

Toubat, Omar; Han, Jason J; Predina, Jarrod D; Goldberg, Lee R; Ibrahim, Michael E.

Afiliación

Toubat O; Division of Cardiovascular Surgery, Department of Surgery, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
Han JJ; Division of Cardiovascular Surgery, Department of Surgery, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
Predina JD; Division of Thoracic Surgery, Department of Surgery, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
Goldberg LR; Division of Cardiovascular Medicine, Department of Medicine, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
Ibrahim ME; Division of Cardiovascular Surgery, Department of Surgery, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.

JACC Case Rep ; 29(10): 102322, 2024 May 15.

Article en En | MEDLINE | ID: mdl-38601846

ABSTRACT

ABSTRACT

Uhl anomaly is characterized by the morphologic absence of right ventricular myocardium and is an exceedingly rare cause of nonischemic cardiomyopathy. We report the first case of a successful heart transplantation in a 41-year-old patient who presented in cardiogenic shock from Uhl anomaly causing decompensated right ventricular failure.

Palabras clave

Uhl anomaly; cardiac transplantation; heart failure

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