[A newborn with a tumour on the tongue and alveolar ridge]. / Een pasgeborene met een afwijking op de tong en kaak.

In a newborn boy, a tumour was seen on the tongue and mandibula. A diagnosis of congenital epulis was made. This usually pedunculated tumour is present at birth and located on the maxillary or mandibular alveolar ridge (more commonly on the maxilla), but rarely on the tongue. It varies greatly in size from just a few millimetres in diameter to several centimetres. Treatment is only necessary when feeding problems occur.

Congenital peripheral developing odontoma accompanied by congenital teratomatous fibroma in a 9-month-old boy: a case report.

Peripheral odontoma is rare, and only two cases of congenital peripheral odontoma have been reported. Congenital oral fibroma is also rare. We describe a unique case of congenital peripheral developing odontoma accompanied by congenital teratomatous fibroma in an infant. Both tumors were difficult to detect on radiography. Two small masses were seen in the median anterior portion of the palatal mucosa of a 9-month-old boy. The masses had been present since birth and were surgically removed at age 28 months, when one of the masses had grown to a diameter of 8 mm. Histopathologic examination showed a fibrous lesion and a tooth germ-like rounded lesion composed of dental papilla, enamel organ, dentin, and cementum. Although congenital odontoma is rare, it should be considered when selecting appropriate treatment, as early radiographic detection is difficult.

Bilateral mandibular hamartomas and familial natal teeth.

The case of a newborn girl with two mandibular incisor natal teeth and bilateral mandibular odontogenic harmartomas is presented. The hamartomas were evident as pedunculated masses on the posterior mandibular gum pads. The natal teeth were extracted at birth, and the hamartomas were excised at 5 months of age. Microscopic investigation of the hamartoma demonstrated the presence of all odontogenic tissues with the exception of an enamel organ. In addition, there was a strong family history of natal teeth, which may suggest a hereditary basis for the development of the odontogenic hamartoma.

Multifocal congenital hemangiopericytomas associated with Kasabach-Merritt syndrome.

A newborn male with multifocal congenital hemangiopericytomas complicated by Kasabach-Merritt syndrome was treated by excision of a large hemangiopericytoma in the right mandibular area. After excision of this lesion, the associated consumptive coagulopathy abated. Spontaneous regression of other subcutaneous tumours over the thighs and left flank was noted by age 6 months; this illustrates the benign course of most congenital hemangiopericytomas. Surgical excision of congenital hemangiopericytoma is indicated when there is a coexisting consumptive coagulopathy or for the definitive control of large lesions. For smaller lesions and in the absence of Kasabach-Merritt syndrome, the benign nature and predilection for spontaneous regression of congenital hemangiopericytomas render observation as the preferred strategy.

Lymphangiomas of the alveolar ridge in a neonate: report of case.

Two alveolar ridge lymphangiomas in a black neonate were identified. No case of neonatal lymphangioma in a non-black has been reported. The majority of treatments for lymphangiomas have been either surgical removal or allowing for spontaneous regression. Both treatments were tried in this case with equal success. The treatment of choice may be to allow for spontaneous regression with periodic monitoring, if the lesion is not endangering the child, thus avoiding surgery.

Multiple congenital epulis of the alveolar ridge and tongue.

Congenital granular cell tumor, also known as congenital epulis, is a very rare lesion seen in newborns. The typical presentation is a solitary nodule occurring on the gingiva of the anterior alveolar ridge of either jaw. Multiple-site involvement is seen very seldom but has been noted on the same or different alveolar ridges. However, tongue involvement is exceptional, and there have been only three cases reported involving both the alveolus and the tongue. A female newborn with multiple congenital epulis on the mandibular alveolar ridge and tongue is presented, and her preferred treatment and histopathological diagnosis are discussed.

Simultaneous occurrence of dermoid and heterotopic intestinal cysts in the floor of the mouth of a newborn.

Congenital cysts of the floor of the mouth are rare. The simultaneous appearance in a newborn of two different types of epithelial-lined cysts is reported. It is the first such case to be reported in the literature.

Congenital osteolipoma of the skull.

A unique case of congenital osteolipoma of the skull occurred. A 27-year-old woman had multiple hard tumors affecting the frontal and parietal bones, the rim of the orbit, the maxilla, the base of the skull, and the horizontal part of the mandible on the right side. The slowly growing tumor was first noticed in the right parietal bone when she was born. The partially excised right frontoparietal lesion was composed of deformed and sclerotic trabeculae of bone and mature adipose tissue that formed an osteolipoma, which was regarded as hamartomatous. Its pathogenesis was suggested as associated with maldifferentiation of the mesenchyme or its derivatives toward the osseous and adipose tissue at the early development of the cranium.