[Conjunctival epithelial carcinoma in a 9-year-old child with xeroderma pigmentosum. Case report]. / Epithelioma conjonctival chez un enfant de neuf ans porteur d'un Xeroderma Pigmentosum. A propos d'un cas.

ABSTRACT

We report the case of a conjunctival tumor in a 9-year-old patient, suffering from Xeroderma Pigmentosum. Our patient presented a raspberry-colored conjunctival tumor. The tumor was resecked without any additional treatment. The histological study revealed squamous cell carcinoma. A suspicion of relapse appeared two months later of the same location and a new resection was performed. The initial checkup of this tumor was negative. In this disease, ocular localizations are frequent. The conjunctiva, the cornea, the eyelids and, into a lesser extent, the orbit can be involved. Basal cell carcinoma and squamous cell carcinoma are the most frequent tumors observed in Xeroderma Pigmentosum. Their treatment is mainly surgical.