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Real-world assessment of LCI following lumacaftor-ivacaftor initiation in adolescents and adults with cystic fibrosis.
Reix, Philippe; Tatopoulos, Aurélie; Ioan, Iulia; Le Bourgeois, Muriel; Bui, Stéphanie; Choukroun, Marie Luce; Bessaci-Kabouya, Katia; Gerardin, Michele; Bokov, Plamen; Da Silva, Jennifer; Paillasseur, Jean-Louis; Burgel, Pierre Regis.
Afiliación
  • Reix P; Cystic Fibrosis Center, Hospices Civils de Lyon, Lyon, France; UMR 5558 CNRS Equipe EMET Université Claude Bernard Lyon 1 Lyon, France. Electronic address: philippe.reix@chu-lyon.fr.
  • Tatopoulos A; Pediatric Cystic Fibrosis Center, Hôpital d'Enfants, Centre Hospitalier Universitaire de Nancy, Nancy, France.
  • Ioan I; Service d'Explorations Fonctionnelles Pédiatriques, Hôpital d'Enfants, Centre Hospitalier Universitaire de Nancy, Nancy, France.
  • Le Bourgeois M; Pediatric Respiratory Disease and Cystic Fibrosis Center National Reference Cystic Fibrosis Reference Center, Hôpital Universitaire Necker Enfants Malades, Paris, France.
  • Bui S; Pediatric Respiratory Disease and Cystic Fibrosis Center and CIC 1401, CHU de Bordeaux, Bordeaux, France.
  • Choukroun ML; Service d'explorations fonctionnelles respiratoires pédiatriques, CHU de Bordeaux, Bordeaux, France.
  • Bessaci-Kabouya K; Department of Pediatrics A and Cystic Fibrosis Center, American Memorial Hospital, Reims, France.
  • Gerardin M; Pediatric Cystic Fibrosis center, Hôpital Robert Debré, AP-HP, Paris, France.
  • Bokov P; Service de Physiologie Pédiatrique, AP-HP, Hôpital Robert Debré, Paris, France; Université de Paris, UMR1141, Equipe NeoPhen, INSERM co-tutelle, Paris, France.
  • Da Silva J; Université de Paris, Institut Cochin, Inserm, Paris U1016, France; ERN-Lung CF network, France; URC-CIC Paris Descartes Necker Cochin, AP-HP, Hôpital Cochin, Paris, France.
  • Paillasseur JL; Effi-stat, Paris, France.
  • Burgel PR; Université de Paris, Institut Cochin, Inserm, Paris U1016, France; ERN-Lung CF network, France; Respiratory Medicine and National Cystic Fibrosis Reference Center, Cochin Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France.
J Cyst Fibros ; 21(1): 155-159, 2022 01.
Article en En | MEDLINE | ID: mdl-34183285

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Quinolonas / Fibrosis Quística / Benzodioxoles / Aminofenoles / Aminopiridinas Tipo de estudio: Etiology_studies / Incidence_studies / Observational_studies / Risk_factors_studies Límite: Adolescent / Humans Idioma: En Revista: J Cyst Fibros Año: 2022 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Quinolonas / Fibrosis Quística / Benzodioxoles / Aminofenoles / Aminopiridinas Tipo de estudio: Etiology_studies / Incidence_studies / Observational_studies / Risk_factors_studies Límite: Adolescent / Humans Idioma: En Revista: J Cyst Fibros Año: 2022 Tipo del documento: Article