Search details
1.
mtUPR Modulation as a Therapeutic Target for Primary and Secondary Mitochondrial Diseases.
Int J Mol Sci
; 24(2)2023 Jan 12.
Article
in English
| MEDLINE | ID: mdl-36674998
2.
Antioxidants Prevent Iron Accumulation and Lipid Peroxidation, but Do Not Correct Autophagy Dysfunction or Mitochondrial Bioenergetics in Cellular Models of BPAN.
Int J Mol Sci
; 24(19)2023 Sep 26.
Article
in English
| MEDLINE | ID: mdl-37834028
3.
Vitamin E prevents lipid peroxidation and iron accumulation in PLA2G6-Associated Neurodegeneration.
Neurobiol Dis
; 165: 105649, 2022 04.
Article
in English
| MEDLINE | ID: mdl-35122944
4.
Coenzyme Q10: Novel Formulations and Medical Trends.
Int J Mol Sci
; 21(22)2020 Nov 10.
Article
in English
| MEDLINE | ID: mdl-33182646
5.
Vicious cycle of lipid peroxidation and iron accumulation in neurodegeneration.
Neural Regen Res
; 18(6): 1196-1202, 2023 Jun.
Article
in English
| MEDLINE | ID: mdl-36453394
6.
Neurodegeneration, Mitochondria, and Antibiotics.
Metabolites
; 13(3)2023 Mar 12.
Article
in English
| MEDLINE | ID: mdl-36984858
7.
Alpha-lipoic acid supplementation corrects pathological alterations in cellular models of pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels.
Orphanet J Rare Dis
; 18(1): 80, 2023 04 12.
Article
in English
| MEDLINE | ID: mdl-37046296
8.
Patient-Derived Cellular Models for Polytarget Precision Medicine in Pantothenate Kinase-Associated Neurodegeneration.
Pharmaceuticals (Basel)
; 16(10)2023 Sep 26.
Article
in English
| MEDLINE | ID: mdl-37895830
9.
Mitochondrial Quality Control via Mitochondrial Unfolded Protein Response (mtUPR) in Ageing and Neurodegenerative Diseases.
Biomolecules
; 13(12)2023 12 13.
Article
in English
| MEDLINE | ID: mdl-38136659
10.
Actin Polymerization Defects Induce Mitochondrial Dysfunction in Cellular Models of Nemaline Myopathies.
Antioxidants (Basel)
; 12(12)2023 Nov 21.
Article
in English
| MEDLINE | ID: mdl-38136143
11.
Therapeutic approach with commercial supplements for pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels.
Orphanet J Rare Dis
; 17(1): 311, 2022 08 09.
Article
in English
| MEDLINE | ID: mdl-35945593
12.
Pantothenate and L-Carnitine Supplementation Improves Pathological Alterations in Cellular Models of KAT6A Syndrome.
Genes (Basel)
; 13(12)2022 12 06.
Article
in English
| MEDLINE | ID: mdl-36553567
13.
Pterostilbene in Combination With Mitochondrial Cofactors Improve Mitochondrial Function in Cellular Models of Mitochondrial Diseases.
Front Pharmacol
; 13: 862085, 2022.
Article
in English
| MEDLINE | ID: mdl-35370630
14.
Activation of the Mitochondrial Unfolded Protein Response: A New Therapeutic Target?
Biomedicines
; 10(7)2022 Jul 06.
Article
in English
| MEDLINE | ID: mdl-35884915
15.
UPRmt activation improves pathological alterations in cellular models of mitochondrial diseases.
Orphanet J Rare Dis
; 17(1): 204, 2022 05 17.
Article
in English
| MEDLINE | ID: mdl-35581596
16.
Down regulation of the expression of mitochondrial phosphopantetheinyl-proteins in pantothenate kinase-associated neurodegeneration: pathophysiological consequences and therapeutic perspectives.
Orphanet J Rare Dis
; 16(1): 201, 2021 05 05.
Article
in English
| MEDLINE | ID: mdl-33952316
17.
From Mitochondria to Atherosclerosis: The Inflammation Path.
Biomedicines
; 9(3)2021 Mar 05.
Article
in English
| MEDLINE | ID: mdl-33807807
18.
Mitochondria and Antibiotics: For Good or for Evil?
Biomolecules
; 11(7)2021 07 17.
Article
in English
| MEDLINE | ID: mdl-34356674
19.
Coenzyme Q10 Analogues: Benefits and Challenges for Therapeutics.
Antioxidants (Basel)
; 10(2)2021 Feb 04.
Article
in English
| MEDLINE | ID: mdl-33557229
20.
Advances in mt-tRNA Mutation-Caused Mitochondrial Disease Modeling: Patients' Brain in a Dish.
Front Genet
; 11: 610764, 2020.
Article
in English
| MEDLINE | ID: mdl-33510772