1.
World J Pediatr Congenit Heart Surg
; : 21501351241236720, 2024 May 02.
Artículo
en Inglés
| MEDLINE
| ID: mdl-38693789
RESUMEN
Uhl's anomaly is a rare congenital syndrome characterized by the absence of right ventricular myocardium. The widely accepted pathological mechanism is intrauterine myocardial apoptosis. Uhl's syndrome carries a poor prognosis. In rare situations, patients with Uhl's anomaly reach adulthood. We will present a case of a 29-year-old patient with Uhl's syndrome treated at our center, highlighting the diagnostic, surgical, and postoperative challenges in management.