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Abnormal type I collagen post-translational modification and crosslinking in a cyclophilin B KO mouse model of recessive osteogenesis imperfecta.
Cabral, Wayne A; Perdivara, Irina; Weis, MaryAnn; Terajima, Masahiko; Blissett, Angela R; Chang, Weizhong; Perosky, Joseph E; Makareeva, Elena N; Mertz, Edward L; Leikin, Sergey; Tomer, Kenneth B; Kozloff, Kenneth M; Eyre, David R; Yamauchi, Mitsuo; Marini, Joan C.
Affiliation
  • Cabral WA; Bone and Extracellular Matrix Branch, NICHD, NIH, Bethesda, Maryland, United States of America.
  • Perdivara I; Laboratory of Structural Biology, NIEHS, NIH, Research Triangle Park, North Carolina, United States of America.
  • Weis M; Orthopaedic Research Laboratories, University of Washington, Seattle, Washington, United States of America.
  • Terajima M; North Carolina Oral Health Institute, University of North Carolina, Chapel Hill, Chapel Hill, North Carolina, United States of America.
  • Blissett AR; Bone and Extracellular Matrix Branch, NICHD, NIH, Bethesda, Maryland, United States of America.
  • Chang W; Bone and Extracellular Matrix Branch, NICHD, NIH, Bethesda, Maryland, United States of America.
  • Perosky JE; Orthopaedic Research Laboratories, Department of Orthopaedic Surgery, University of Michigan, Ann Arbor, Michigan, United States of America.
  • Makareeva EN; Section on Physical Biochemistry, NICHD, NIH, Bethesda, Maryland, United States of America.
  • Mertz EL; Section on Physical Biochemistry, NICHD, NIH, Bethesda, Maryland, United States of America.
  • Leikin S; Section on Physical Biochemistry, NICHD, NIH, Bethesda, Maryland, United States of America.
  • Tomer KB; Laboratory of Structural Biology, NIEHS, NIH, Research Triangle Park, North Carolina, United States of America.
  • Kozloff KM; Orthopaedic Research Laboratories, Department of Orthopaedic Surgery, University of Michigan, Ann Arbor, Michigan, United States of America.
  • Eyre DR; Orthopaedic Research Laboratories, University of Washington, Seattle, Washington, United States of America.
  • Yamauchi M; North Carolina Oral Health Institute, University of North Carolina, Chapel Hill, Chapel Hill, North Carolina, United States of America.
  • Marini JC; Bone and Extracellular Matrix Branch, NICHD, NIH, Bethesda, Maryland, United States of America.
PLoS Genet ; 10(6): e1004465, 2014 Jun.
Article in En | MEDLINE | ID: mdl-24968150

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Osteogenesis Imperfecta / Protein Processing, Post-Translational / Cyclophilins / Collagen Type I Limits: Animals / Humans / Male Language: En Journal: PLoS Genet Journal subject: GENETICA Year: 2014 Type: Article Affiliation country: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Osteogenesis Imperfecta / Protein Processing, Post-Translational / Cyclophilins / Collagen Type I Limits: Animals / Humans / Male Language: En Journal: PLoS Genet Journal subject: GENETICA Year: 2014 Type: Article Affiliation country: United States