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Bioenergetic status modulates motor neuron vulnerability and pathogenesis in a zebrafish model of spinal muscular atrophy.
Boyd, Penelope J; Tu, Wen-Yo; Shorrock, Hannah K; Groen, Ewout J N; Carter, Roderick N; Powis, Rachael A; Thomson, Sophie R; Thomson, Derek; Graham, Laura C; Motyl, Anna A L; Wishart, Thomas M; Highley, J Robin; Morton, Nicholas M; Becker, Thomas; Becker, Catherina G; Heath, Paul R; Gillingwater, Thomas H.
Afiliación
  • Boyd PJ; Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom.
  • Tu WY; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Shorrock HK; Sheffield Institute for Translation Neuroscience, University of Sheffield, Sheffield, United Kingdom.
  • Groen EJN; Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom.
  • Carter RN; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Powis RA; Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom.
  • Thomson SR; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Thomson D; University/British Heart Foundation Centre for Cardiovascular Science, University of Edinburgh, Queens Medical Research Institute, Edinburgh, United Kingdom.
  • Graham LC; Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom.
  • Motyl AAL; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Wishart TM; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Highley JR; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Morton NM; Division of Neurobiology, Roslin Institute, University of Edinburgh, Edinburgh, United Kingdom.
  • Becker T; Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom.
  • Becker CG; Division of Neurobiology, Roslin Institute, University of Edinburgh, Edinburgh, United Kingdom.
  • Heath PR; Sheffield Institute for Translation Neuroscience, University of Sheffield, Sheffield, United Kingdom.
  • Gillingwater TH; University/British Heart Foundation Centre for Cardiovascular Science, University of Edinburgh, Queens Medical Research Institute, Edinburgh, United Kingdom.
PLoS Genet ; 13(4): e1006744, 2017 04.
Article en En | MEDLINE | ID: mdl-28426667

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Fosfoglicerato Quinasa / Médula Espinal / Atrofia Muscular Espinal / Proteína 1 para la Supervivencia de la Neurona Motora / Neuronas Motoras Tipo de estudio: Etiology_studies Límite: Animals / Humans Idioma: En Revista: PLoS Genet Asunto de la revista: GENETICA Año: 2017 Tipo del documento: Article País de afiliación: Reino Unido

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Fosfoglicerato Quinasa / Médula Espinal / Atrofia Muscular Espinal / Proteína 1 para la Supervivencia de la Neurona Motora / Neuronas Motoras Tipo de estudio: Etiology_studies Límite: Animals / Humans Idioma: En Revista: PLoS Genet Asunto de la revista: GENETICA Año: 2017 Tipo del documento: Article País de afiliación: Reino Unido