Mass spectrometric quantification of plasma glycosphingolipids in human GM3 ganglioside deficiency.
Clin Mass Spectrom
; 14 Pt B: 106-114, 2019 Nov.
Article
en En
| MEDLINE
| ID: mdl-34917767
CID, collision-induced dissociation; Cer, ceramide; Dp, degree of polymerization; EGCase, endoglycosylceramidase; ESI-MS, electrospray ionization mass spectrometry; GD3, disialo-ganglioside GD3 (IUPAC-IUB: II3- α -(Neu5Ac)2-Gg2Cer); GM1b, monosialo-ganglioside GM1b (IUPAC-IUB: IV3-α-Neu5Ac-Gg4Cer); GM3; GM3, monosialo-ganglioside GM3; GSL, glycosphingolipid; Gal, galactose; GalNAc, N-acetylgalactosamine; Ganglioside; Gb3, globotriaosylceramide (IUPAC-IUB: Gb3Cer); Gb3-D, deuterated Gb3; Gb4, globotetraosylceramide (IUPAC-IUB: Gb4Cer); Glc, glucose; GlcCer, glucosylceramide; Glycosphingolipid; LacCer, lactosylceramide; MS, mass spectrometry; MSn, multidimensional mass spectrometry; Mass spectrometry; NL, neutral loss; NSI, nanospray ionization; Neu5Ac, sialic acid as N-5-acetylneuraminic acid; Plasma; ST3GAL5, CMP-Neu5Ac:Lactosylceramide alpha-2,3-sialyltransferase 5, previously known as SIAT9, SIATGM3S, ST3GalV, GM3-synthase; TIM, total ion mapping; UPLC, ultra-high pressure liquid chromatography
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Colección:
01-internacional
Banco de datos:
MEDLINE
Tipo de estudio:
Guideline
Idioma:
En
Revista:
Clin Mass Spectrom
Año:
2019
Tipo del documento:
Article
País de afiliación:
Grecia