[Extra medullary hematopoiesis associated to congenital dyserythropoietic anemia II in adult]. / Hématopoïèse extramédullaire associée à une dysérythropoïèse congénitale II chez l'adulte.
Ann Biol Clin (Paris)
; 70(2): 217-20, 2012.
Article
en Fr
| MEDLINE
| ID: mdl-22484535
ABSTRACT
The congenital dyserythropoietic anemias comprise a group of rare hereditary disorders of erythropoiesis characterized by anemia with ineffective erythropoiesis and morphological abnormalities of erythroblasts in the bone marrow. Congenital dyserythropoietic anemia type II or HEMPAS is the more frequent type. It is rare in adults. Extra medullary hematopoiesis is also a rare entity; it is a physiological response to chronic anemia observed in certain hemopathies like congenital dyserythropoietic anemia type II. We report the observation of a patient for who diagnosis of extra medullary hematopoiesis associated to congenital dyserythropoietic type II was made in adulthood.
Texto completo:
1
Colección:
01-internacional
Banco de datos:
MEDLINE
Asunto principal:
Hematopoyesis Extramedular
/
Anemia Diseritropoyética Congénita
Tipo de estudio:
Diagnostic_studies
/
Etiology_studies
/
Risk_factors_studies
Límite:
Adult
/
Female
/
Humans
/
Middle aged
Idioma:
Fr
Revista:
Ann Biol Clin (Paris)
Año:
2012
Tipo del documento:
Article
País de afiliación:
Túnez