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NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models.
Zulian, Alessandra; Rizzo, Erika; Schiavone, Marco; Palma, Elena; Tagliavini, Francesca; Blaauw, Bert; Merlini, Luciano; Maraldi, Nadir Mario; Sabatelli, Patrizia; Braghetta, Paola; Bonaldo, Paolo; Argenton, Francesco; Bernardi, Paolo.
Afiliación
  • Zulian A; Department of Biomedical Sciences Consiglio Nazionale Delle Ricerche Neuroscience Institute, I-35131 Padova, Italy.
  • Rizzo E; Department of Biomedical Sciences Consiglio Nazionale Delle Ricerche Neuroscience Institute, I-35131 Padova, Italy.
  • Schiavone M; Department of Biology and.
  • Palma E; Department of Biomedical Sciences.
  • Tagliavini F; Laboratory of Musculoskeletal Cell Biology, Istituto Ortopedico Rizzoli, I-40136 Bologna, Italy and.
  • Blaauw B; Department of Biomedical Sciences.
  • Merlini L; Laboratory of Musculoskeletal Cell Biology, Istituto Ortopedico Rizzoli, I-40136 Bologna, Italy and.
  • Maraldi NM; Laboratory of Musculoskeletal Cell Biology, Istituto Ortopedico Rizzoli, I-40136 Bologna, Italy and.
  • Sabatelli P; Laboratory of Musculoskeletal Cell Biology, Istituto Ortopedico Rizzoli, I-40136 Bologna, Italy and Consiglio Nazionale Delle Ricerche, Institute of Molecular Genetics, I-40136 Bologna, Italy.
  • Braghetta P; Department of Molecular Medicine, University of Padova, I-35131 Padova, Italy.
  • Bonaldo P; Department of Molecular Medicine, University of Padova, I-35131 Padova, Italy.
  • Argenton F; Department of Biology and.
  • Bernardi P; Department of Biomedical Sciences Consiglio Nazionale Delle Ricerche Neuroscience Institute, I-35131 Padova, Italy, bernardi@bio.unipd.it.
Hum Mol Genet ; 23(20): 5353-63, 2014 Oct 15.
Article en En | MEDLINE | ID: mdl-24852368

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Ciclosporina / Proteínas de Pez Cebra / Colágeno Tipo VI / Distrofias Musculares Límite: Animals / Humans Idioma: En Revista: Hum Mol Genet Asunto de la revista: BIOLOGIA MOLECULAR / GENETICA MEDICA Año: 2014 Tipo del documento: Article País de afiliación: Italia

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Ciclosporina / Proteínas de Pez Cebra / Colágeno Tipo VI / Distrofias Musculares Límite: Animals / Humans Idioma: En Revista: Hum Mol Genet Asunto de la revista: BIOLOGIA MOLECULAR / GENETICA MEDICA Año: 2014 Tipo del documento: Article País de afiliación: Italia