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Early whole-body mutant huntingtin lowering averts changes in proteins and lipids important for synapse function and white matter maintenance in the LacQ140 mouse model.
Shing, Kai; Sapp, Ellen; Boudi, Adel; Liu, Sophia; Seeley, Connor; Marchionini, Deanna; DiFiglia, Marian; Kegel-Gleason, Kimberly B.
Afiliación
  • Shing K; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Sapp E; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Boudi A; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Liu S; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Seeley C; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Marchionini D; CHDI Management/CHDI Foundation, New York, NY 10001, USA.
  • DiFiglia M; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Kegel-Gleason KB; Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA. Electronic address: kkegelgleason@mgh.harvard.edu.
Neurobiol Dis ; 187: 106313, 2023 Oct 15.
Article en En | MEDLINE | ID: mdl-37777020

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Enfermedad de Huntington / Sustancia Blanca Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Neurobiol Dis Asunto de la revista: NEUROLOGIA Año: 2023 Tipo del documento: Article País de afiliación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Enfermedad de Huntington / Sustancia Blanca Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Neurobiol Dis Asunto de la revista: NEUROLOGIA Año: 2023 Tipo del documento: Article País de afiliación: Estados Unidos