[Amyotrophic lateral sclerosis with deafness: report of a case and review of the literature]. / Esclerose lateral amiotrófica com surdez: relato de um caso e revisão da literatura.

ABSTRACT

A case of chronic bulb-pontine paralysis with deafness, with early onset, coursing along nine years is reported. There seem to be histopathologic and electromyographic evidences on which is concluded to be a variant form of juvenile amyotrophic lateral sclerosis (Van Laere form).