Tailgut cyst adenocarcinoma
Autops. Case Rep
; 10(1): 2019115, Jan.-Mar. 2020. ilus
Article
en En
| LILACS
| ID: biblio-1087653
Biblioteca responsable:
BR26.7
ABSTRACT
Tailgut cysts (TGCs) are rare congenital entities arising from remnants of the embryological postanal primitive gut. Malignancy in TGCs is rare, with the majority being adenocarcinomas and carcinoid tumors. A search of the published literature yielded only 27 cases of adenocarcinoma developing in TGCs. We described the case of a 54-year-old female who presented with complaints of pelvic and perineal pain of several weeks. After the initial work-up, a mass in the right presacral location was diagnosed. She underwent radical resection of the tumor, using a posterior approach. The lesion was removed en bloc with the middle rectum, coccyx, and sacrum (S4S5). The histopathologic examination revealed an adenocarcinoma arising in a TGC, and the patient received adjuvant chemoradiotherapy. Our case underlines that diagnosing a TGC is difficult as it is a rare congenital lesion. Clinical examination may be challenging as TGCs present with various symptoms, which can mimic other commonly proctologic disorders. Patients should be referred to a tertiary center with experience in pelvic surgery and must be managed by a multidisciplinary approach to maximize successful treatment. The recommended treatment is surgical excision given the malignant potential of TGCs and their risk of causing local complications.
Palabras clave
Texto completo:
1
Base de datos:
LILACS
Asunto principal:
Neoplasias Pélvicas
/
Quistes
Límite:
Female
/
Humans
Idioma:
En
Revista:
Autops. Case Rep
/
Autopsy and Case Reports
Asunto de la revista:
Anatomia
/
Patologia Cl¡nica
/
Patologia Legal
Año:
2020
Tipo del documento:
Article
País de afiliación:
Portugal