[Susac's syndrome: improvement with combined cyclophosphamide and intravenous immunoglobulin therapy]. / Syndrome de Susac: un cas d'évolution favorable sous cyclophosphamide et immunoglobulines intraveineuses.
Rev Neurol (Paris)
; 156(8-9): 783-5, 2000 Sep.
Article
en Fr
| MEDLINE
| ID: mdl-10992124
ABSTRACT
We report a case of Susac's syndrome characterized by subacute encephalopathy, bilateral hearing loss and multiple bilateral branch retinal artery occlusions in a forty-year-old-white-woman. Brain Magnetic Resonance Imaging showed on T2-weighted images multiple, punctate areas of increased signal intensity in periventricular white matter, gray matter and brainstem most of them being enhanced by gadolinium. Cerebrospinal fluid was acellular but with an increased protein level (1.66 g/l). Treatment with cyclophosphamid and intravenous immmunoglobulin resulted in dramatic improvement of the clinical status over the following months and CSF normalization.
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Base de datos:
MEDLINE
Asunto principal:
Arteriopatías Oclusivas
/
Encéfalo
/
Encefalopatías
/
Inmunoglobulinas Intravenosas
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Ciclofosfamida
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Pérdida Auditiva Sensorineural
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Inmunosupresores
Límite:
Adult
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Female
/
Humans
Idioma:
Fr
Revista:
Rev Neurol (Paris)
Año:
2000
Tipo del documento:
Article