Pulmonary Hypertension Associated with Anti-synthetase Syndrome: A Case Report and Literature Review.
Intern Med
; 62(24): 3685-3689, 2023 Dec 15.
Article
en En
| MEDLINE
| ID: mdl-37062737
ABSTRACT
Pulmonary hypertension (PH) is a serious condition in which there is an abnormally high pressure in the pulmonary arteries that can occur as a complication of connective tissue diseases. Although the relationship between PH and systemic lupus erythematosus or systemic sclerosis has been well-characterized, PH rarely occurs in patients with anti-synthetase syndrome (ASS), and little is known about the pathophysiology and clinical outcome of patients with ASS-PH. We herein report a patient with anti-Jo-1-positive ASS complicated by PH and discuss the treatment strategy through a review of previously reported cases.
Palabras clave
Texto completo:
1
Base de datos:
MEDLINE
Asunto principal:
Esclerodermia Sistémica
/
Enfermedades del Tejido Conjuntivo
/
Hipertensión Pulmonar
/
Lupus Eritematoso Sistémico
Tipo de estudio:
Risk_factors_studies
Límite:
Humans
Idioma:
En
Revista:
Intern Med
Asunto de la revista:
MEDICINA INTERNA
Año:
2023
Tipo del documento:
Article
País de afiliación:
Japón