[Clinical and genetic manifestations of left ventricular non-compaction in children]. / Caratteristiche cliniche e genetiche del ventricolo sinistro non compatto in età pediatrica.
G Ital Cardiol (Rome)
; 25(2): 98-105, 2024 Feb.
Article
en It
| MEDLINE
| ID: mdl-38270365
ABSTRACT
Left ventricular non-compaction (LVNC) is a myocardial disease characterized by a two-layered structure typically seen at the apical and lateral left portions of the ventricular myocardium, distal to the papillary muscles. While considered a rare disease, its prevalence in children is increasing due to the increased awareness of this condition and improved resolution of imaging techniques. The etiology is heterogeneous, ranging from inherited conditions to acquired diseases. Although many patients are asymptomatic, some patients may experience adverse events, including heart failure, arrhythmias, or thromboembolic events. Several echocardiographic or cardiac magnetic resonance imaging diagnostic criteria have been proposed for diagnosing LVNC. However, their application in children is significantly limited. This review aims to describe the clinical and genetic characteristics of children with LVNC and discuss the role of the proposed diagnostic criteria.
Texto completo:
1
Base de datos:
MEDLINE
Asunto principal:
Insuficiencia Cardíaca
/
Ventrículos Cardíacos
Tipo de estudio:
Risk_factors_studies
Límite:
Child
/
Humans
Idioma:
It
Revista:
G Ital Cardiol (Rome)
/
G. ital. cardiol. (2006, Online)
/
Giornale italiano di cardiologia (2006, Online)
Asunto de la revista:
CARDIOLOGIA
Año:
2024
Tipo del documento:
Article