Detalhe da pesquisa
1.
Genotype, oxidase status, and preceding infection or autoinflammation do not affect allogeneic HCT outcomes for CGD.
Blood
; 142(24): 2105-2118, 2023 12 14.
Artigo
em Inglês
| MEDLINE | ID: mdl-37562003
2.
Posttransplantation late complications increase over time for patients with SCID: A Primary Immune Deficiency Treatment Consortium (PIDTC) landmark study.
J Allergy Clin Immunol
; 153(1): 287-296, 2024 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-37793572
3.
Allogeneic hematopoietic cell transplantation is effective for p47phox chronic granulomatous disease: A Primary Immune Deficiency Treatment Consortium study.
J Allergy Clin Immunol
; 153(5): 1423-1431.e2, 2024 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-38290608
4.
Quercetin ameliorates XIAP deficiency-associated hyperinflammation.
Blood
; 140(7): 706-715, 2022 08 18.
Artigo
em Inglês
| MEDLINE | ID: mdl-35687753
5.
Intestinal microbiome and metabolome signatures in patients with chronic granulomatous disease.
J Allergy Clin Immunol
; 152(6): 1619-1633.e11, 2023 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-37659505
6.
The 2022 EULAR/ACR points to consider at the early stages of diagnosis and management of suspected haemophagocytic lymphohistiocytosis/macrophage activation syndrome (HLH/MAS).
Ann Rheum Dis
; 82(10): 1271-1285, 2023 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-37487610
7.
T-cell activation profiles distinguish hemophagocytic lymphohistiocytosis and early sepsis.
Blood
; 137(17): 2337-2346, 2021 04 29.
Artigo
em Inglês
| MEDLINE | ID: mdl-33512385
8.
Excessive IL-10 and IL-18 trigger hemophagocytic lymphohistiocytosis-like hyperinflammation and enhanced myelopoiesis.
J Allergy Clin Immunol
; 150(5): 1154-1167, 2022 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-35792218
9.
Comparison of hematopoietic cell transplant conditioning regimens for hemophagocytic lymphohistiocytosis disorders.
J Allergy Clin Immunol
; 149(3): 1097-1104.e2, 2022 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-34375618
10.
Preemptive hematopoietic cell transplantation for asymptomatic patients with X-linked lymphoproliferative syndrome type 1.
Clin Immunol
; 237: 108993, 2022 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-35367395
11.
Reduced-Intensity/Reduced-Toxicity Conditioning Approaches Are Tolerated in XIAP Deficiency but Patients Fare Poorly with Acute GVHD.
J Clin Immunol
; 42(1): 36-45, 2022 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34586554
12.
Granulocyte Transfusions in Patients with Chronic Granulomatous Disease Undergoing Hematopoietic Cell Transplantation or Gene Therapy.
J Clin Immunol
; 42(5): 1026-1035, 2022 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-35445907
13.
Pediatric hemophagocytic lymphohistiocytosis.
Blood
; 135(16): 1332-1343, 2020 04 16.
Artigo
em Inglês
| MEDLINE | ID: mdl-32107531
14.
Model-informed precision dosing for alemtuzumab in paediatric and young adult patients undergoing allogeneic haematopoietic cell transplantation.
Br J Clin Pharmacol
; 88(1): 248-259, 2022 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34182590
15.
Test-dose pharmacokinetics guided melphalan dose adjustment in reduced intensity conditioning allogeneic transplant for non-malignant disorders.
Br J Clin Pharmacol
; 88(1): 115-127, 2022 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34075614
16.
Relationship Between Severity of T Cell Lymphopenia and Immune Dysregulation in Patients with DiGeorge Syndrome (22q11.2 Deletions and/or Related TBX1 Mutations): a USIDNET Study.
J Clin Immunol
; 41(1): 29-37, 2021 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-32949294
17.
Experience with a Reduced Toxicity Allogeneic Transplant Regimen for Non-CGD Primary Immune Deficiencies Requiring Myeloablation.
J Clin Immunol
; 41(1): 89-98, 2021 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-33067658
18.
α4ß7 Integrin expression and blockade in pediatric and young adult gastrointestinal graft-versus-host disease.
Pediatr Blood Cancer
; 68(8): e28968, 2021 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-33861521
19.
CD38brightCD8+ T Cells Associated with the Development of Acute GVHD Are Activated, Proliferating, and Cytotoxic Trafficking Cells.
Biol Blood Marrow Transplant
; 26(1): 1-6, 2020 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-31442594
20.
Thinking Beyond HLH: Clinical Features of Patients with Concurrent Presentation of Hemophagocytic Lymphohistiocytosis and Thrombotic Microangiopathy.
J Clin Immunol
; 40(5): 699-707, 2020 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-32447592