Detalhe da pesquisa
1.
Correction of cilia structure and function alleviates multi-organ pathology in Bardet-Biedl syndrome mice.
Hum Mol Genet
; 29(15): 2508-2522, 2020 08 29.
Artigo
em Inglês
| MEDLINE | ID: mdl-32620959
2.
Reduction of ciliary length through pharmacologic or genetic inhibition of CDK5 attenuates polycystic kidney disease in a model of nephronophthisis.
Hum Mol Genet
; 25(11): 2245-2255, 2016 06 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-27053712
3.
CaMKII as a pathological mediator of ER stress, oxidative stress, and mitochondrial dysfunction in a murine model of nephronophthisis.
Am J Physiol Renal Physiol
; 310(11): F1414-22, 2016 06 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-27076647
4.
Inhibition of TGF-ß Increases Bone Volume and Strength in a Mouse Model of Osteogenesis Imperfecta.
JBMR Plus
; 5(9): e10530, 2021 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-34532615
5.
Inhibition of glucosylceramide accumulation results in effective blockade of polycystic kidney disease in mouse models.
Nat Med
; 16(7): 788-92, 2010 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-20562878
6.
Pkd1 and Nek8 mutations affect cell-cell adhesion and cilia in cysts formed in kidney organ cultures.
Am J Physiol Renal Physiol
; 294(1): F73-83, 2008 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-17928412
7.
Development of polycystic kidney disease in juvenile cystic kidney mice: insights into pathogenesis, ciliary abnormalities, and common features with human disease.
J Am Soc Nephrol
; 17(10): 2821-31, 2006 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-16928806
8.
Impaired formation of desmosomal junctions in ADPKD epithelia.
Histochem Cell Biol
; 124(6): 487-97, 2005 Dec.
Artigo
em Inglês
| MEDLINE | ID: mdl-16187067
9.
Canine PKD1 is a single-copy gene: genomic organization and comparative analysis.
Genomics
; 80(1): 105-12, 2002 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-12079289
10.
New insights into ADPKD molecular pathways using combination of SAGE and microarray technologies.
Genomics
; 84(3): 497-510, 2004 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-15498457