1.
Arq Bras Cardiol
; 75(3): 243-8, 2000 Sep.
Artigo
em Inglês, Português
| MEDLINE
| ID: mdl-11018810
RESUMO
Total generalized lipodystrophy (Berardinelli - Seip Syndrome) is a rare hereditary disease characterized by insulin-resistant diabetes mellitus and a small quantity of adipose tissue and is of unknown origin. Common cardiovascular alterations related to this syndrome are cardiac hypertrophy and arterial hypertension. This article reports a case of Berardinelli - Seip syndrome and reviews the literature with special emphasis on the cardiovascular manifestations of this syndrome.