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Liver disease predicts mortality in patients with X-linked immunodeficiency with hyper-IgM but can be prevented by early hematopoietic stem cell transplantation.
Azzu, Vian; Kennard, Lucinda; Morillo-Gutierrez, Beatriz; Slatter, Mary; Edgar, J David M; Kumararatne, Dinakantha S; Griffiths, William J H.
Afiliação
  • Azzu V; Liver Unit, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom.
  • Kennard L; Department of Allergy, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom.
  • Morillo-Gutierrez B; Department of Paediatric Immunology, Great North Children's Hospital, Newcastle upon Tyne, United Kingdom.
  • Slatter M; Department of Paediatric Immunology, Great North Children's Hospital, Newcastle upon Tyne, United Kingdom.
  • Edgar JDM; Regional Immunology Service, Royal Victoria Hospital, The Belfast Health & Social Care Trust, Belfast, United Kingdom.
  • Kumararatne DS; Department of Immunology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom.
  • Griffiths WJH; Liver Unit, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom. Electronic address: bill.griffiths@addenbrookes.nhs.uk.
J Allergy Clin Immunol ; 141(1): 405-408.e7, 2018 01.
Article em En | MEDLINE | ID: mdl-28756297

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Transplante de Células-Tronco Hematopoéticas / Síndrome de Imunodeficiência com Hiper-IgM Tipo 1 / Hepatopatias Idioma: En Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Reino Unido

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Transplante de Células-Tronco Hematopoéticas / Síndrome de Imunodeficiência com Hiper-IgM Tipo 1 / Hepatopatias Idioma: En Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Reino Unido