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Atxn2-CAG100-KnockIn mouse spinal cord shows progressive TDP43 pathology associated with cholesterol biosynthesis suppression.
Canet-Pons, Júlia; Sen, Nesli-Ece; Arsovic, Aleksandar; Almaguer-Mederos, Luis-Enrique; Halbach, Melanie V; Key, Jana; Döring, Claudia; Kerksiek, Anja; Picchiarelli, Gina; Cassel, Raphaelle; René, Frédérique; Dieterlé, Stéphane; Fuchs, Nina V; König, Renate; Dupuis, Luc; Lütjohann, Dieter; Gispert, Suzana; Auburger, Georg.
Afiliação
  • Canet-Pons J; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany.
  • Sen NE; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany; Faculty of Biosciences, Goethe University, 60438 Frankfurt am Main, Germany.
  • Arsovic A; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany.
  • Almaguer-Mederos LE; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany; Center for Investigation and Rehabilitation of Hereditary Ataxias (CIRAH), Holguín, Cuba.
  • Halbach MV; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany.
  • Key J; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany; Faculty of Biosciences, Goethe University, 60438 Frankfurt am Main, Germany.
  • Döring C; Dr. Senckenberg Institute of Pathology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany.
  • Kerksiek A; Institute of Clinical Chemistry and Clinical Pharmacology, University Hospital Bonn, 53127 Bonn, Nordrhein-Westfalen, Germany.
  • Picchiarelli G; UMRS-1118 INSERM, Faculty of Medicine, University of Strasbourg, 67000 Strasbourg, France.
  • Cassel R; UMRS-1118 INSERM, Faculty of Medicine, University of Strasbourg, 67000 Strasbourg, France.
  • René F; UMRS-1118 INSERM, Faculty of Medicine, University of Strasbourg, 67000 Strasbourg, France.
  • Dieterlé S; UMRS-1118 INSERM, Faculty of Medicine, University of Strasbourg, 67000 Strasbourg, France.
  • Fuchs NV; Host-Pathogen Interactions, Paul-Ehrlich-Institute, 63225 Langen, Germany.
  • König R; Host-Pathogen Interactions, Paul-Ehrlich-Institute, 63225 Langen, Germany.
  • Dupuis L; UMRS-1118 INSERM, Faculty of Medicine, University of Strasbourg, 67000 Strasbourg, France.
  • Lütjohann D; Institute of Clinical Chemistry and Clinical Pharmacology, University Hospital Bonn, 53127 Bonn, Nordrhein-Westfalen, Germany.
  • Gispert S; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany.
  • Auburger G; Experimental Neurology, Medical Faculty, Goethe University, 60590 Frankfurt am Main, Germany. Electronic address: auburger@em.uni-frankfurt.de.
Neurobiol Dis ; 152: 105289, 2021 05.
Article em En | MEDLINE | ID: mdl-33577922

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Medula Espinal / Colesterol / Ataxias Espinocerebelares / Proteinopatias TDP-43 Idioma: En Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Alemanha

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Medula Espinal / Colesterol / Ataxias Espinocerebelares / Proteinopatias TDP-43 Idioma: En Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Alemanha