ABSTRACT
BACKGROUND: Some congenital heart diseases are compatible with early life presenting their peculiar challenges in adulthood. Some of them are particularly rare, and are misdiagnosed in the absence of modern imaging facilities. Intra - cardiac aneurysms fall into this group. OBJECTIVE: The clinical presentation of the cases up to point of sudden death were documented and echocardiography done. RESULTS: Two such cases which were never encountered in over 20 years of echocardiography in our unit are reported. One was a ruptured sinus of Valsalva aneurysm dissecting the interventricular septum and the other ventricular septal defect aneurysm involving the tricuspid valve. CONCLUSION: Some congenital heart diseases present late. Increased availability of echocardiography and skilled personnel should lead to early diagnosis preventing fatality that follows late diagnosis as occurred here.