RESUMEN
Mobius syndrome is a rare condition of unclear origin, characterized by a unilateral or bilateral congenital facial weakness with impairment of ocular abduction, which is frequently associated with limb anomalies . Poland described a condition in which there was unilateral absence of pectoralis major muscle and ipsilateral syndactyly. The combination of Poland-Mobius syndrome is rare, with an estimated prevalence 1:500 000. We describe a case of Poland-Mobius syndrome in association with congenital bilateral vocal fold immobility. To our knowldge, this is the first report of such an association between Poland-Mobius syndrome and congenital bilateral vocal fold immobility.
Asunto(s)
Síndrome de Mobius/fisiopatología , Síndrome de Poland/fisiopatología , Parálisis de los Pliegues Vocales/etiología , Femenino , Humanos , Recién Nacido , Síndrome de Mobius/complicaciones , Síndrome de Poland/complicaciones , Parálisis de los Pliegues Vocales/congénitoRESUMEN
OBJECTIVES: To demonstrate the technique and efficacy of powered assisted adenoidectomy using nasal endoscopy. PATIENTS AND METHODS: Between 2002 and 2003, forty children (age ranged from 3 to 17 years) with symptoms and signs suggestive of snoring and/or obstructive sleep apnea and choanal adenoids were randomly selected and distributed in two groups. Group A underwent transnasal endoscopic powered adenoidectomy (TEPA) and group B underwent curettage adenoidectomy (CA). Both groups underwent pre- and postoperative nasal endoscopy. Direct comparisons between the two groups were made with regards to operative time, amount of blood loss, postoperative morbidity, complications, and resolution of symptoms. RESULTS: Male to female distribution was equal 1:1. The mean age of both groups was 8 years. In group A, the mean blood loss was 8.2 ml compared to 22.1 ml in group B (p<0.05). The operative time in group A was 6.1 min vs 12.3 min in group B (p<0.05). There were no operative or postoperative complications in both groups. Postoperative follow up and nasal endoscopy showed no recurrence of symptoms or adenoid remnants. CONCLUSION: Using TEPA for removing choanal adenoids is an adequate and safe method. The TEPA technique can be added to the armamentarium of techniques used by pediatric otolaryngologists.
Asunto(s)
Adenoidectomía/métodos , Tonsila Faríngea/cirugía , Atresia de las Coanas/cirugía , Endoscopía/métodos , Nariz/cirugía , Tonsila Faríngea/patología , Adolescente , Niño , Preescolar , Atresia de las Coanas/fisiopatología , Femenino , Estudios de Seguimiento , Humanos , Hipertrofia/patología , Hipertrofia/cirugía , Tiempo de Internación , Masculino , Procedimientos Quirúrgicos Mínimamente Invasivos/métodos , Dolor Postoperatorio/fisiopatología , Cuidados Posoperatorios , Cuidados Preoperatorios , Estudios Prospectivos , Medición de Riesgo , Resultado del TratamientoRESUMEN
OBJECTIVE: To obtain baseline data on the most common surgical emergencies in pediatric otolaryngology in Saudi Arabia. METHODS: This report is a retrospective study of all children presenting to the pediatric otolaryngology emergency service at King Abdulaziz University Hospital in Riyadh, Kingdom of Saudi Arabia. Between January 2001 to January 2006 data were carefully collected and then analyzed for patients requiring emergent surgical intervention by the pediatric otolaryngology service. RESULTS: A total of 15,850 children presented to our pediatric otolaryngology emergency service. Surgical intervention was indicated in 183 children (1.2%). The larynx/head & neck was the most common site involved. Foreign body related emergencies were the most common presentation requiring surgical interventions (42%). The aero-digestive tract was the most common site for foreign body retrieval (54%). CONCLUSION: Pediatric patients have always constituted a significant portion of the general otolaryngology service. Most pediatric otolaryngology emergencies are relatively benign. Aero-digestive tract foreign bodies are the most common indication for surgical intervention in ped iatric otolaryngology.