Detalhe da pesquisa
1.
PERK inhibition delays neurodegeneration and improves motor function in a mouse model of Marinesco-Sjögren syndrome.
Hum Mol Genet
; 27(14): 2477-2489, 2018 07 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-29718201
2.
Cyclophillin A deficiency accelerates RML-induced prion disease.
Neurobiol Dis
; 130: 104498, 2019 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-31181281
3.
Transgenic fatal familial insomnia mice indicate prion infectivity-independent mechanisms of pathogenesis and phenotypic expression of disease.
PLoS Pathog
; 11(4): e1004796, 2015 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-25880443
4.
A tetracationic porphyrin with dual anti-prion activity.
iScience
; 26(9): 107480, 2023 Sep 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-37636075
5.
Erratum: A tetracationic porphyrin with dual anti-prion activity.
iScience
; 26(11): 108223, 2023 Nov 17.
Artigo
em Inglês
| MEDLINE | ID: mdl-37915608
6.
Transgenic mice recapitulate the phenotypic heterogeneity of genetic prion diseases without developing prion infectivity: Role of intracellular PrP retention in neurotoxicity.
Prion
; 10(2): 93-102, 2016 03 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-26864450