RESUMO
The Wissler-Fanconi syndrome is an inflammatory disease of unknown origin, similar to Still's disease, a systemic form of juvenile arthritis. The long-term evolution is marked by recurrent febrile exacerbations, sometimes complicated by pericardo-myocarditis which usually resolves without sequellae. The authors report a case with chronic pericardo-myocarditis progressing over a 7 year period to refractory congestive cardiac failure.
Assuntos
Miocardite/etiologia , Pericardite/etiologia , Síndrome de Wissler/complicações , Adulto , Cardiopatias/etiologia , Humanos , Masculino , Fatores de Tempo , Síndrome de Wissler/diagnósticoAssuntos
Doença de Still de Início Tardio , Síndrome de Wissler , Corticosteroides/uso terapêutico , Adulto , Fatores Etários , Criança , Pré-Escolar , Diagnóstico Diferencial , Feminino , Humanos , Lactente , Masculino , Fatores Sexuais , Doença de Still de Início Tardio/diagnóstico , Síndrome de Wissler/diagnóstico , Síndrome de Wissler/tratamento farmacológicoAssuntos
Síndrome de Wissler , Criança , Pré-Escolar , Feminino , Humanos , Lactente , Masculino , Síndrome de Wissler/diagnóstico , Síndrome de Wissler/terapiaAssuntos
Hipersensibilidade a Drogas/diagnóstico , Síndrome de Wissler/diagnóstico , Adulto , Aspirina/efeitos adversos , Diagnóstico Diferencial , Difenidramina/efeitos adversos , Dipirona/efeitos adversos , Hipersensibilidade a Drogas/etiologia , Emergências , Feminino , Humanos , Doença Iatrogênica , Sulfadimetoxina/efeitos adversos , Síndrome de Wissler/induzido quimicamenteAssuntos
Síndrome de Wissler/diagnóstico , Adolescente , Artrite Juvenil/diagnóstico , Artrite Reumatoide/diagnóstico , Diagnóstico Diferencial , Humanos , Lúpus Eritematoso Sistêmico/diagnóstico , Masculino , Paraproteinemias/diagnóstico , Doença de Raynaud/diagnóstico , Toxoplasmose/diagnóstico , Yersiniose/diagnósticoRESUMO
Case report of a baby and his 26-year old mother suffering from Subsepsis allergica. Her disease was discovered when she was 2 years old. Both patients showed common symptoms such as regular bouts of high fever with brief exanthemas resistant to antibiotic treatment. The results of their hematological tests were typical of this illness. The mother has also suffered from sporadic attacks of arthritis for the past ten years, but these have not handicapped her in any way. In spite of extensive diagnostic tests we were unable to shed new light on the etiopathogenesis of this systemic form of chronic juvenile arthritis. Since the baby's illness has so far proved to be of benign nature, long-term medication was found to be unnecessary. The mother finds relief through symptomatic treatment.
Assuntos
Síndrome de Wissler/genética , Adulto , Cefalosporinas/uso terapêutico , Desoxicorticosterona/uso terapêutico , Diagnóstico Diferencial , Antígenos HLA/genética , Humanos , Lactente , Masculino , Síndrome de Wissler/diagnósticoRESUMO
A further case of subsepsis allergica Wissler in a 35-year-old woman is reported. The problems of the differential diagnosis of this rare disease are discussed. In the present case the disease could successfully be controlled using imuran in combination with corticosteroids.