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Enhanced cell-surface stability of rescued DeltaF508 cystic fibrosis transmembrane conductance regulator (CFTR) by pharmacological chaperones.
Varga, Karoly; Goldstein, Rebecca F; Jurkuvenaite, Asta; Chen, Lan; Matalon, Sadis; Sorscher, Eric J; Bebok, Zsuzsa; Collawn, James F.
Affiliation
  • Varga K; Department of Cell Biology, University of Alabama at Birmingham, Birmingham, AL 35294, USA.
Biochem J ; 410(3): 555-64, 2008 Mar 15.
Article in En | MEDLINE | ID: mdl-18052931

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Cystic Fibrosis Transmembrane Conductance Regulator Limits: Animals / Humans Language: En Journal: Biochem J Year: 2008 Type: Article Affiliation country: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Cystic Fibrosis Transmembrane Conductance Regulator Limits: Animals / Humans Language: En Journal: Biochem J Year: 2008 Type: Article Affiliation country: United States