Congenital osteofibrous dysplasia Campanacci: spontaneous postbioptic regression.
J Pediatr Hematol Oncol
; 36(3): 249-52, 2014 Apr.
Article
in En
| MEDLINE
| ID: mdl-23774157
ABSTRACT
Osteofibrous dysplasia Campanacci is a rare benign bone tumor most frequently observed in young childhood. The exclusive localization in the tibia is very characteristic. The incidence of congenital primary bone tumors is an absolute rarity. We report a case of a newborn with a histologically proven osteofibrous dysplasia Campanacci at the tibia presenting a regular radiographic follow-up. After a small open biopsy and spontaneous minor fracture, the lesion rapidly remodeled within 1½ months and almost completely regressed with restutio ad integrum. Surgical intervention in this tumor entity at childhood age has been shown to have a high recurrence rate but due to lack of experience with newborns, guidelines do not exist. We analyze the radiologic and histologic differential diagnosis of juvenile adamantinoma and emphasize that congenital peripheral bone tumors should be treated conservatively when malignancy is excluded.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Tibia
/
Bone Diseases, Developmental
/
Ameloblastoma
/
Jaw Neoplasms
Type of study:
Diagnostic_studies
/
Guideline
/
Prognostic_studies
Limits:
Humans
/
Newborn
Language:
En
Journal:
J Pediatr Hematol Oncol
Journal subject:
HEMATOLOGIA
/
NEOPLASIAS
/
PEDIATRIA
Year:
2014
Type:
Article
Affiliation country:
Germany