Pneumonectomy case in a newborn with congenital pulmonary lymphangiectasia.
J Korean Med Sci
; 29(4): 609-13, 2014 Apr.
Article
in En
| MEDLINE
| ID: mdl-24753713
ABSTRACT
Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ventilator care. Right pneumonectomy was performed after her symptoms worsened. Histologic examination indicated CPL. She is currently 12 months old and developing normally. Pneumonectomy can be considered for treating respiratory symptoms for improving chances of survival in cases with unilateral CPL.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Lung Diseases
/
Lymphangiectasis
Type of study:
Diagnostic_studies
/
Prognostic_studies
Limits:
Female
/
Humans
/
Newborn
Language:
En
Journal:
J Korean Med Sci
Journal subject:
MEDICINA
Year:
2014
Type:
Article