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Recurrent bacterial infections, but not fungal infections, characterise patients with ELANE-related neutropenia: a French Severe Chronic Neutropenia Registry study.
Rotulo, Gioacchino A; Plat, Geneviève; Beaupain, Blandine; Blanche, Stéphane; Moushous, Despina; Sicre de Fontbrune, Flore; Leblanc, Thierry; Renard, Cécile; Barlogis, Vincent; Vigue, Marie-Gabrielle; Freycon, Claire; Piguet, Christophe; Pasquet, Marlène; Fieschi, Claire; Abou-Chahla, Wadih; Gandemer, Virginie; Rialland, Fanny; Millot, Frédéric; Marie-Cardine, Aude; Paillard, Catherine; Levy, Pacifique; Aladjidi, Nathalie; Biosse-Duplan, Martin; Bellanné-Chantelot, Christine; Donadieu, Jean.
Affiliation
  • Rotulo GA; Registre des Neutropénies Chroniques, Centre de Référence des Neutropénies Chroniques, Hôpital Trousseau, Assistance Publique-Hôpitaux de Paris (APHP), Paris, France.
  • Plat G; Department of Neuroscience, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genoa, Italy.
  • Beaupain B; Hématologie Oncologie et Immunologie Pédiatrique, Hôpital des Enfants, Toulouse, France.
  • Blanche S; Registre des Neutropénies Chroniques, Centre de Référence des Neutropénies Chroniques, Hôpital Trousseau, Assistance Publique-Hôpitaux de Paris (APHP), Paris, France.
  • Moushous D; APHP, UIHR CEREDIH, Hôpital Necker-Enfants Malade, Paris, France.
  • Sicre de Fontbrune F; APHP, UIHR CEREDIH, Hôpital Necker-Enfants Malade, Paris, France.
  • Leblanc T; APHP, Service d'Hématologie Transplantation Médullaire, Hôpital Saint-Louis, Paris, France.
  • Renard C; Department of Pediatric Hematology and Immunology, Hôpital Robert-Debré, APHP, Paris, France.
  • Barlogis V; Service de Pédiatrie, Institut d'Hématologie et Oncologie Pédiatrique, Centre Hospitalier Universitaire (CHU) de Lyon, Lyon, France.
  • Vigue MG; Department of Pediatric Hematology, Timone Hospital, Assistance Publique-Hôpitaux de Marseille, Marseille, France.
  • Freycon C; Pediatrics, Infectiology, Rhumatology, Hôpital Arnaud-de-Villeneuve, CHRU de Montpellier, Montpellier, France.
  • Piguet C; Service d'Onco-Hématologie Pédiatrique, CHU de Grenoble, Grenoble, France.
  • Pasquet M; Service d'Hémato-Oncologie Pédiatrie, CHU de Limoges, Limoges, France.
  • Fieschi C; Hématologie Oncologie et Immunologie Pédiatrique, Hôpital des Enfants, Toulouse, France.
  • Abou-Chahla W; Department of Clinical Immunology, Saint-Louis Hospital, APHP, Paris, France.
  • Gandemer V; Department of Pediatric Hematology, Jeanne-de-Flandre Hospital, CHU de Lille, Lille, France.
  • Rialland F; Service d'Hémato-Oncologie Pédiatrique, CHU de Rennes, Rennes, France.
  • Millot F; Service d'Oncologie Pédiatrique, CHU de Nantes, Nantes, France.
  • Marie-Cardine A; Service d'Hémato-Oncologie Pédiatrique, CHU de Poitiers, Poitiers, France.
  • Paillard C; Service d'Hémato-Pédiatrique, CHU de Rouen, Rouen, France.
  • Levy P; Service d'Hématologie Oncologie Pédiatrique, CHU de Strasbourg, Strasbourg, France.
  • Aladjidi N; Département de Génétique, DMU BioGeM, CHU Pitié-Salpêtrière, APHP, Sorbonne Université, Paris, France.
  • Biosse-Duplan M; Service d'Hémato-Oncologie Pédiatrique, CHU de Bordeaux, Bordeaux, France.
  • Bellanné-Chantelot C; Service de Médecine Bucco-Dentaire, Hôpital Bretonneau, APHP, Paris, France.
  • Donadieu J; Département de Génétique, DMU BioGeM, CHU Pitié-Salpêtrière, APHP, Sorbonne Université, Paris, France.
Br J Haematol ; 194(5): 908-920, 2021 09.
Article in En | MEDLINE | ID: mdl-34340247

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Bacterial Infections / Leukocyte Elastase / Mycoses / Neutropenia Type of study: Observational_studies / Prognostic_studies / Risk_factors_studies Limits: Adolescent / Adult / Child / Humans / Infant Country/Region as subject: Europa Language: En Journal: Br J Haematol Year: 2021 Type: Article Affiliation country: France

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Bacterial Infections / Leukocyte Elastase / Mycoses / Neutropenia Type of study: Observational_studies / Prognostic_studies / Risk_factors_studies Limits: Adolescent / Adult / Child / Humans / Infant Country/Region as subject: Europa Language: En Journal: Br J Haematol Year: 2021 Type: Article Affiliation country: France